A Rare Case of a Large Meningocele Posterior Sacrococcygeal

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  •   Rakotondraibe Willy Francis

  •   Bemora Joseph Synèse

  •   Habib Nouraly

  •   Raveloharimino Nirina Henintsoa

  •   Tsiaremby Marc Guichard

  •   Rabesandratana Norotiana

  •   Andrianarimanana Diavolana

  •   Andriamamonjy Clément

Abstract

We report a case of sacrococcygeal meningocele simulating a sacrococcygeal teratoma. Likewise, there are a discussion of the pathophysiology and surgical approach of these types of lesions. We present a case of an exceptionally large posterior coccygeal meningocele of a newborn, and show the interest of radio-echographic couple and the interest of a management surgical approach. This was a case of posterior coccygeal meningocele, in a 10-day-old newborn born at term, with no known maternal history other than active smoking. The clinical examination finds a eupneic newborn, presents a median mass at the level of the sacrococcygeal part, of soft consistency, painless, without signs of inflammation, of normal skin, volume 18 x 21 x 19 cm, with positive transillumination test, no sensitivomotor deficit of both limbs, no other malformative anomalies detected clinically, but presence of anal atony and vesico-anal inconstancy. The ultrasound reveals a fluid formation containing small cysts. The x-ray revealed the absence of the posterior coccyx arch, an appearance in favor of a posterior sacrococcygeal meningocele. The surgery consisted of a meningocele cure followed by a buttock plasty. The postoperative follow-up was simple, without infectious or metabolic complications. Standardization and improvement of accessibility to ultrasound and obstetric MRI could improve the antenatal diagnosis of this pathology in Madagascar.
 


Keywords: closed spinal bifida, méningocèle, surgery x-ray computed

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How to Cite
Francis, R. W., Synèse, B. J., Nouraly, H., Henintsoa, R. N., Guichard, T. M., Norotiana, R., Diavolana, A., & Clément, A. (2021). A Rare Case of a Large Meningocele Posterior Sacrococcygeal. European Journal of Clinical Medicine, 2(1), 20–22. https://doi.org/10.24018/clinicmed.2021.2.1.17

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