A Case Report on Budd Chiari Syndrome – Which Mimics Multiple Disorders

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  •   Niveditha Dileep

  •   John Thomas

  •   Jisha James

  •   Abhijith V

Abstract

Background: Budd Chiari Syndrome (BCS) is the king of disorders which will mimic other disorders like chronic biliary disease, constrictive pericarditis, sinusoidal obstruction syndrome and so on, as it be like that, it is less diagnosed and treated in many countries. The prevalence of BCS is one in one million population, so it is a very rare case therefore it should be treated properly because many disorders like hematologic or malignant disease are the complications of BCS [1], [2].


Objective: To access the clinical variants of BCS along with the similarities and differences in clinical presentation, diagnostic approaches, and general treatment pattern which mimic, BCS thus gives the physician a clear outline about those disorders.


Method: A man of 42 years old having BCS was taken for the study to carry out the differences in clinical features of BCS which distinguish the mimicking disorders. Clinical presentations were noted. Laboratory tests and diagnostic tests showed that the patient is having comorbidities including fatty liver with cholelithiasis, mild splenomegaly, liver parenchyma diseases, large esophageal varies with signs of recent hemorrhage, port hypertensive gastropathy and minimal ascites [3]. Patient get discharged after feeling better.


Result: This patient is having chronic BCS with DIPS dysfunction. The patient had no history of liver disease before diagnosing BCS. BCS is almost curable when it is diagnosed correctly as early as possible. If not diagnosed early and treated well, comorbidities will occur, and it will affect the patient quality of life.


Discussion: Early detection and proper treatment will help to control the disease up to an extent. This is depending on the physician’s knowledge. Hence, this case study clearly explains the disorders which mimic BCS for better understanding.


Keywords: Budd Chiari Syndrome, constrictive pericarditis, chronic biliary disease, veno occlusive disorder

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How to Cite
Dileep, N., Thomas, J., James, J., & V, A. (2021). A Case Report on Budd Chiari Syndrome – Which Mimics Multiple Disorders. European Journal of Clinical Medicine, 2(3), 4–7. https://doi.org/10.24018/clinicmed.2021.2.3.64